Online ISSN: 2515-8260

Keywords : primary ciliary dyskinesia

SYNDROME KARTAGENER IN CHILDREN (clinical case of observation)

I.A. Dauksh; A.L. Aliev; G.S. Shaislamova; G. Z. Pirnazarova; Y.Sh. Maxkamova

European Journal of Molecular & Clinical Medicine, 2020, Volume 7, Issue 2, Pages 3102-3111

Primary ciliary dyskinesia (Kartagener syndrome) refers to inherited
rare diseases, characterized by the reverse location of internal organs, the development of
secondary chronic diseases of the bronchi, hypoplasia of the sinuses and the development
of chronic rhino-sinusitis.
In the article the peculiarities of clinic, diagnostics and treatment of children with
the syndrome of Kartagener. A clinical caseof diagnosis of this pathology in a child in the
first year of life is presented.Early diagnosis and regular adequate conservative therapy
contribute to the slow progression of the disease without signs of bronchiectasis.