Pseudocoarctation of the arch and the abdominal aorta: A review
European Journal of Molecular & Clinical Medicine,
2021, Volume 8, Issue 3, Pages 2716-2724
AbstractPseudocoarctaion of the arch of the aorta is a very rare congenital anomaly, occurring in isolation or with other congenital heart diseases. The anatomical basis of the condition is linked to an elongated, redundant aorta which may affect the arch, and very rarely the abdominal aorta giving rise to kink and buckling without causing any significant functional stenosis. It should be carefully differentiated from the more common true coarctation of the aorta. Although asymptomatic in the majority, few patients can have nonspecific symptoms and or complications due to aneurysm formation, dissection, or rupture of the aorta. Hence Pseudocoarctaion should be closely followed for the onset of symptoms or possible complications. In the absence of recommendations, no specific therapy is indicated in asymptomatic patients, although symptoms and complications warrant definitive treatment. In this article, we are discussing embryology, anatomical basis, signs, symptoms, complications, treatment options, and follow-up of patients with pseudocoarctation of the aorta.
Conclusion:Pseudocoarctation of the arch and abdominal aorta is an extremely rare congenital anomaly occurring in isolation or associated with other congenital heart diseases. No clinical features are specific to this condition and often diagnosed incidentally. Although, in the absence of symptoms no therapy is required, the occurrence of symptoms and complications guide definitive therapy. As the natural history of the disease is unknown, the condition when diagnosed should be closely followed up for the occurrence of any complications such as aneurysm formation, dissection, or rupture of the aorta.
- Article View: 67
- PDF Download: 28